Unusual case of visceral metastatic osteolytic giant myxopapillary ependymoma: Report and literature review

Robles Díaz J.F. · Neurologia Argentina (2023) · DOI: 10.1016/j.neuarg.2022.07.008

Resumen

Myxopapillary ependymoma (ME) is a rare tumor of glial lineage that predominantly affects young adults, with an incidence of 0.08 cases per 100,000 people. ME of the conus medullaris, cauda equina, and filum terminale of the spinal cord are generally considered slow-growing, benign tumors. Occasionally, ME can extend to the sacral bones, making it difficult to determine whether the tumor is of intradural or extradural origin. They are generally confined to the spinal canal and the destruction of bony, vertebral or iliac structures adjacent to the tumor are extremely rare events, as are visceral metastatic lesions. Our case had a voluminous lesion at the level of the sacrum with extensive involvement, with visceral dissemination. A biopsy was performed followed by radiotherapy with a locally stationary result, but continued to progress systemically. We have discussed the clinical presentation, radiological features, and management strategies of this disease.

Instituciones: Universidad Peruana Los Andes