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Solid pseudopapillary pancreatic neoplasm in a patient with hereditary hemorrhagic telangiectasia

Alburqueque-Melgarejo J.; Beltrán-Gárate B.; Palomino-Portilla E.A.; Quiñones-Ávila M.D.P.; Quiñones-Laveriano D.M. · Gaceta Mexicana de Oncologia (2024) · DOI: 10.24875/j.gamo.23000036

Resumen

Solid pseudopapillary neoplasm is an extremely rare tumor that represents approximately 0.9-2.7% of all exocrine pancreatic tumors.This entity tends to have a greater predilection for young women between the ages of 18 and 35 and usually presents as a slow-growing abdominal mass with nonspecific manifestations. Its proper diagnosis consists mainly of imaging studies since it presents characteristics that distinguish it from other entities. Likewise, its management requires a multidisciplinary approach, where surgery has shown to play a crucial role.

Instituciones: Universidad Ricardo Palma