Orbital presentation of Rosai-Dorfman disease

Yataco-Vicente, J.A.; Araujo-Castillo, R.V.; López Fuentes, M.H. · Universidad Peruana de Ciencias Aplicadas (UPC) (2018) · DOI: 10.1016/j.oftal.2018.05.006

Resumen

Objective: To report a case of orbital mass and proptosis, diagnosed as Rosai-Dorfman disease (RDD). Methods: Clinical case report based on the review of clinical charts, radiological images, and histopathology. Results: A 42-year-old male with orbital mass and proptosis of the right eye. A surgical biopsy was performed, and the diagnosis of RDD was established using microscopy and immunohistochemistry. Definitive management included open tumour cytoreduction, with good response. Discussion: The RDD is a rare, benign, proliferative condition of unknown origin. It rarely affects the cranial cavities, with the orbital presentation being very unusual. Diagnostic confirmation is essential for the best surgical management.

Instituciones: Universidad Peruana de Ciencias Aplicadas