Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review

León-Palacios J.L.; Palacios M. A.M.; Casavilca-Zambrano S.; Esteban-Arias D.; Sánchez A. S.E.; Wesley Alaba G.; Pineda G. R.A. · Revista de Neuro-Psiquiatria (2020) · DOI: 10.20453/rnp.v83i3.3800

Resumen

Low-grade fibromyxoid sarcoma (LGFMS) is a soft tissue tumor of mesenchymal origin. Sarcomas are a heterogeneous group, representing 1% of all neoplasm diagnoses. Primary sarcomas of the central nervous system (CNS) are rare, and represent only 0.7% of all sarcomas, with an estimated incidence of 3 per 10 million people per year. The case of a 59-year-old woman who developed a low-grade intracranial fibromyxoid sarcoma in the right parietal region, is described. The clinical course, imaging studies, histopathological features, and treatment approach of this unusual diagnosis, are discussed. Low-grade intracranial fibromyxoid sarcoma is a rare and probably under-reported condition. The definitive diagnosis is usually made through histo-pathological studies. © The Author(s), 2020.

Instituciones: Universidad Nacional Mayor de San Marcos; Universidad Nacional Federico Villarreal; Universidad de Huánuco