Intracranial Rosai-Dorfman disease: an infrequent differential diagnosis for meningioma. Report of a case

Castro-Castillo E.; Macha-Quillama L.; León-Palacios J.; Salas-Dueñas Y.; Lovatón-Espadín R. · Acta Medica Peruana (2023) · DOI: 10.35663/amp.2023.401.2503

Resumen

Rosai-Dorfman disease is an infrequent condition with no known etiology. The intracranial presentation is even rarer, and it resembles the appearance of a meningioma in image studies. We present the case of a 38-year-old male patient who was admitted because of an extra-axial supratentorial cranial tumor, associated to mild neurological deficit. The presumptive diagnosis was convexity meningioma. After surgery, the definitive histologic diagnosis was intracranial Rosai-Dorfman disease. This condition should be considered in the differential diagnosis of an extra-axial intracranial lesion suggesting meningioma, because of similar neuroimaging results and the similar clinical picture.