Hemoperitoneum secondary to a malignant tumor of the sheath of the peripheral nerve in the liver

Chávez-Sánchez S.A.; Bellido Caparó Á.; García Encinas C.A.; Gallegos Serruto G.S.; Bravo Taxa M.D.P.; Vásquez Morales V.M. · Revista de gastroenterologia del Peru : organo oficial de la Sociedad de Gastroenterologia del Peru (2024)

Resumen

Malignant peripheral nerve sheath tumors are frequently associated with neurofibromatosis type 1. They are usually located in the extremities or in the axial area. Its visceral location is very rare and its hepatic origin is infrequent. They tend to be aggressive with a poor response to chemotherapy and radiotherapy, so surgical management is the best treatment option. We present the case of a young man with neurofibromatosis type 1, who presented with hemoperitoneum as a complication of a malignant tumor of the peripheral nerve sheath located in the liver.

Instituciones: Universidad Peruana Cayetano Heredia