Atypical presentation of ruptured right sinus of Valsalva aneurysm with severe aortic insufficiency

Serrano-Sánchez M.Á.; Sotomayor-Estrada A.; Cubas W.S. · Archivos Peruanos de Cardiologia y Cirugia Cardiovascular (2023) · DOI: 10.47487/apcyccv.v4i2.284

Resumen

The sinus of Valsalva aneurysm (SVA) is a rare abnormality that affects less than 0.1% of the general population. We present the case of a 37-year-old woman with a clinical picture characterized by dyspnea, palpitations, and syncope of 6 years of evolution. The echocardiographic study revealed a right SVA with a subpulmonary interventricular perforation of 8mm, resulting in a regurgitant jet into the right ventricle. This led to the dilatation of the right ventricular outflow tract, pulmonary artery, and severe aortic insufficiency (Carpentier’s ID). The patient underwent a successful repair of the defect and interventricular perforation, and valve replacement was not required. Timely echocardiographic diagnosis and early surgery are the main predictors that make the difference between an excellent outcome and certain death.